Autoimmune encephalitis accompanied with status epilepticus, dyskinesia and hypoventilation syndrome: A case report and literature review

WANG Qinying; GU Qin; YU Min; JIANG Dudu; ZHAN Qing

doi:10.12022/jnnr.2017-0021

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Journal of Neurology and Neurorehabilitation ›› 2017, Vol. 13 ›› Issue (2) : 98-103. DOI: 10.12022/jnnr.2017-0021

Autoimmune encephalitis accompanied with status epilepticus, dyskinesia and hypoventilation syndrome: A case report and literature review

WANG Qinying1, 2, GU Qin1, 2, YU Min1, 2, JIANG Dudu1, 2, ZHAN Qing1, 2

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Abstract

Objective: To summarize the clinical features of autoimmune encephalitis so as to reduce the clinical misdiagnosis. Methods: The diagnosis and treatment and the follow-up data of a young female patient with autoimmune encephalitis were reviewed retrospectively. Results: The patient had a fever as the initial symtom and the disease progressed rapidly with status epilepsy, motor disorders and hypoventilation syndrome. Immunotherapy was administered when the diagnosis of autoimmune encephalitis was confirmed. At the third month since the onset of the disease, the condition of the patient was gradually improved; at the fifteenth month, the patient achieved good prognosis. Conclusion: In clinical practice, a young patient with mental disorders, dyskinesia and epilepsy suspected of autoimmune encephalitis should receive detection of serum antibodies associated with autoimmune encephalitis and the cerebrospinal fluid test to make a definite diagnosis.

Key words

Encephalitis / Autoimmune encephalitis / Status epilepticus / Motor disorders

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WANG Qinying, GU Qin, YU Min, JIANG Dudu, ZHAN Qing. Autoimmune encephalitis accompanied with status epilepticus, dyskinesia and hypoventilation syndrome: A case report and literature review[J]. Journal of Neurology and Neurorehabilitation. 2017, 13(2): 98-103 https://doi.org/10.12022/jnnr.2017-0021

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Funding

Youth Fund Project of Science and Technology Commission of Shanghai Municipality (No. 20164Y0073); Academic Research Project of Shanghai University of Traditional Chinese Medicine (No. 2016YG36); Course Construction Project of Shanghai University of Traditional Chinese Medicine (No. SHUTCMKCJSY2016090); Talents Training Program of Seventh People’s Hospital Affiliated to Shanghai University of Traditional Chinese Medicine (No. MZY2017-01)